Observing a brain scan

Hemangioblastoma

Minimally invasive keyhole surgery is now possible for most Hemangioblastomas

Hemangioblastomas are benign brain tumors that most often arise in the cerebellum or brainstem.

Symptomatic hemangioblastomas generally require surgical removal. At Pacific BTC, we have a large experience treating these tumors with minimally invasive keyhole approaches.

By incorporating cutting edge technology and instrumentation with proven surgical experience, we make hemangioblastoma surgery safer, less invasive and more effective.

Learn more about our multidisciplinary team

Overview

These relatively uncommon benign tumors are comprised of blood vessels and typically arise in the cerebellum, but can also occur in the brainstem and spinal cord.

They typically have a solid and a cystic component. Hemangioblastomas may also occur in patients with Von Hippel-Lindau disease, an inherited autosomal dominant condition in which both benign and malignant tumors develop including retinal angiomas, pancreatic cysts, pheochromocytoma and renal cell carcinoma.

Symptoms

Patients with a cerebellar hemangioblastoma typically develop symptoms related to the enlarging tumor and cyst putting pressure on the cerebellum or causing hydrocephalus (excess cerebrospinal fluid).

Common symptoms include headache, loss of coordination, imbalance, nausea and vomiting. Brainstem and spinal cord hemangioblastomas may cause loss of motor function (weakness), and loss of sensation in the extremities or impaired bowel and bladder function.

Diagnosis

Hemangioblastomas are typically diagnosed by MRI of the brain or spinal cord. A CT scan of the brain will also identify most cerebellar and brainstem hemangioblastomas.

The solid part of the hemangioblastoma (mural nodule) enhances intensely after contrast administration on both MRI and CT while the associated cyst (fluid) does not enhance.

Treatment

Symptomatic cerebellar or brainstem hemangioblastomas are typically treated by surgical removal through a sub-occipital or Retromastoid Craniotomy. The goal of hemangioblastoma surgery is to remove the enhancing tumor nodule completely which is able to be accomplished in 80-90% of patients.

For partially removed tumors, radiosurgery or stereotactic radiotherapy is relatively effective. Any patient diagnosed with a hemangioblastoma should have a thorough evaluation for Von Hippel-Lindau disease.


Doctors and Specialists Who Treat Hemangioblastomas

Written and reviewed by:
We are a highly specialized team of medical professionals with extensive neurological and cranial disorder knowledge, expertise and writing experience.
Last updated: January 12, 2023